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The journal «ONCOSURGERY» 2013, Vol.5, No 1

Ewing’s sarcoma metastasis in petrosal bone

Stepanyan MA, Cherekaev VA, Kushel YuV, Rotin DL

NN Burdenko Research Institute of Neurosurgery, RAMS, Moscow, Russia
Contact: Stepanyan Musheg Agoevich, e-mail:

Ewing Sarcoma (ES) is second malignant tumor of bones, but it rarely occurs in cranial bones. Currently, because of discovering of the identical entity not only in bones but also in soft tissues, the term «Tumor of ES family» is used. Maximum of ‘classic bone’ ES incidence occurs between age of 5 and 13, and the tumor has an aggressive behavior, distant metastases develop frequently. In the same time, one should differ between metastatic ES in cranium base, representing advanced stage of oncologic process, and primary ES of cranial bones, which has even more favorable prognosis than when locating in long bones.

Detailed description of two cases of metastatic ES in petrosal bone is presented. The problems of clinical, instrumental and laboratory diagnosis, as well combined approaches to the treatment, differential diagnosis aspects and prognostic factors, are discussed. Review of corresponding references is given.

KEY WORDS: Ewing’s sarcoma, skull base.


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